Suffering from rare Wilsons disease girl in coma undergoes lifesaving liver transplant
New Delhi Apr 19 PTI An 8-year-old girl from Bihar underwent a lifesaving liver transplant procedure here after being diagnosed with a rare disease which has a 100 per cent mortality rate in children who develop coma Indraprastha Apollo Hospitals said on TuesdayWilsons disease is a genetic disorder in which excess copper builds up in the body leading to liver damage Its treatment includes lifelong medication to bind copper However some children develop coma due to liver failure it saidAnshika was admitted to Indraprastha Apollo Hospitals on March 25 in a state of coma the hospital said in a statement adding that she was being treated at another hospital where her condition had deterioratedThe child was immediately put on a ventilator and advised a liver transplantShe was parallely put on dialysis and plasma exchange therapy to remove copper and buy time for a pre-transplant evaluation the hospital addedDue to non-availability of the same or compatible blood group donor an ABO-incompatible emergency live donor liver transplant was planned with the childs mother as the donor it addedWithin 36 hours of admission on March 27 liver transplantation was done Anupam Sibal Group Medical Director and Senior Pediatric Gastroenterologist saidThe complexity of the case required us to support the child on ventilator immediately post her admission Both her pre-surgical management and the seamless administration of the liver transplant surgery with her donor being ABO Compatible were a challenge he saidOf the 432 pediatric liver transplants performed at the Apollo Liver Transplant Programme this is the first case of an emergency ABO-incompatible living related liver transplant he addedTwo days later the child was removed from the ventilator and she regained consciousnessNeerav Goyal senior consultant Liver Transplant at Indraprastha Apollo Hospitalssaid A rare complication in case of Wilsons disease children typically manifest deteriorating symptoms and if not treated within a specific duration can cause life threatening problems This child had come to us with acute liver failure swelling in the brain due to ammonia content was unconscious and in a state of coma At Apollo we immediately counselled the family for a liver transplant Her recovery has been uneventful and the child was discharged on April 12 post-operative day 17 he saidPTI VA PLB SRY
New Delhi Apr 19 PTI An 8-year-old girl from Bihar underwent a lifesaving liver transplant procedure here after being diagnosed with a rare disease which has a 100 per cent mortality rate in children who develop coma Indraprastha Apollo Hospitals said on TuesdayWilsons disease is a genetic disorder in which excess copper builds up in the body leading to liver damage Its treatment includes lifelong medication to bind copper However some children develop coma due to liver failure it saidAnshika was admitted to Indraprastha Apollo Hospitals on March 25 in a state of coma the hospital said in a statement adding that she was being treated at another hospital where her condition had deterioratedThe child was immediately put on a ventilator and advised a liver transplantShe was parallely put on dialysis and plasma exchange therapy to remove copper and buy time for a pre-transplant evaluation the hospital addedDue to non-availability of the same or compatible blood group donor an ABO-incompatible emergency live donor liver transplant was planned with the childs mother as the donor it addedWithin 36 hours of admission on March 27 liver transplantation was done Anupam Sibal Group Medical Director and Senior Pediatric Gastroenterologist saidThe complexity of the case required us to support the child on ventilator immediately post her admission Both her pre-surgical management and the seamless administration of the liver transplant surgery with her donor being ABO Compatible were a challenge he saidOf the 432 pediatric liver transplants performed at the Apollo Liver Transplant Programme this is the first case of an emergency ABO-incompatible living related liver transplant he addedTwo days later the child was removed from the ventilator and she regained consciousnessNeerav Goyal senior consultant Liver Transplant at Indraprastha Apollo Hospitalssaid A rare complication in case of Wilsons disease children typically manifest deteriorating symptoms and if not treated within a specific duration can cause life threatening problems This child had come to us with acute liver failure swelling in the brain due to ammonia content was unconscious and in a state of coma At Apollo we immediately counselled the family for a liver transplant Her recovery has been uneventful and the child was discharged on April 12 post-operative day 17 he saidPTI VA PLB SRY
